Chiari Malformation
Chiari Malformation
The Chiari malformations consists of four types of hindbrain abnormalities, probably unrelated to each other. The majority of Chiari malformations are types 1 or 2. It is a heterogeneous group of conditions, with the underlying commonality of disruption of normal CSF flow through the foramen magnum (FM). It may be congenital or acquired. Cerebellar tonsillar herniation on MRI: criteria vary, > 5mm below the foramen magnum is often cited, but is neither essential nor diagnostic of the condition. Treatment, when indicated, is surgical.
Sign & Symptom of Paediatric Chiari Malformation
- Respiratory difficulties
- Lower cranial nerve palsies.
- Aspiration pneumonia
- Spina bifida
- Nystagmus
- Retrocollis
- Spasticity
- Gait ataxia
- Dissociated sensory loss and spastic quadraparesis